What is situs ambiguus?
Heterotaxy (or situs ambiguus) is defined as the abnormal arrangement of thoracic or abdominal organs, or both, across the left-right axis (Video 90.1.
Is dextrocardia the same as situs inversus?
Situs inversus with dextrocardia is also termed situs inversus totalis because the cardiac position, as well as the atrial chambers and abdominal viscera, is a mirror image of the normal anatomy.
What is a situs abnormality?
Situs anomalies represent a spectrum of disorders in which there is a failure to develop the normal pattern of body asymmetry and which are associated with intestinal rotational disorder [1]. The control of normal human somatic asymmetry is not yet known.
What is the difference between heterotaxy and situs inversus?
Situs inversus totalis involves the complete transposition of all visceral organs, while heterotaxy (situs ambiguus) is used to describe any deviation from the standard placement of organs in the abdomen.
What is atrial situs solitus?
Situs solitus is the medical term referring to the normal position of thoracic and abdominal organs. Anatomically, this means that the heart is on the left with the pulmonary atrium on the right and the systemic atrium on the left along with the cardiac apex.
What is Situs levocardia?
Situs solitus (rare plural: sitūs soliti) refers to the normal position of the thoracic and abdominal organs. This will include a left-sided heart, also known as levocardia.
How long can you live with heterotaxy?
Survival for patients with heterotaxy syndrome was 83% over a median follow-up of 65 months.
How common is situs Ambiguus?
Situs ambiguus is a rare congenital defect in which the major visceral organs are distributed abnormally within the chest and abdomen.
How rare is it to have your heart on the right side?
Dextrocardia is a rare heart condition in which your heart points toward the right side of your chest instead of the left side. Dextrocardia is congenital, which means people are born with this abnormality. Less than 1 percent of the general population is born with dextrocardia.
What is Dextrocardia with situs solitus?
In dextrocardia with situs solitus, the abdominal organs are in normal configuration, but the heart is located in the right hemithorax. 1 The majority of patients with this condition have significant cardiac disorders; only 10% of patients with dextrocardia with situs solitus are free from significant cardiac pathology.
What is the pathophysiology of situs ambiguus?
Due to abnormal cardiac development, patients with situs ambiguus usually develop right atrial isomerism consisting of two bilaterally paired right atria, or left atrial isomerism consisting of two bilaterally paired left atria.
What is dextrocardia and how is it diagnosed?
Dextrocardia is a congenital abnormality in which the heart is positioned in the right hemithorax. To classify the diagnosis, the situs type must be determined. The word situs refers to the arrangement of structures within the human body, and the 3 types are situs solitus, situs inversus, and situs ambiguus.
What is the difference between heterotaxy and situs ambiguus?
Situs ambiguus. Jump to navigation Jump to search. Situs ambiguus is a rare congenital defect in which the major visceral organs are distributed abnormally within the chest and abdomen. Heterotaxy in general refers to any defect of left-right laterality and arrangement of the visceral organs.